Spinal epidural lipomatosis is a rare condition which is described as the accumulation of fat in the extradural territory and often causes dural impingement. Spinal epidural lipomatosis has been implicated in causing a variety of neurologic impairments ranging from back pain, radiculopathy, claudication, myelopathy or even cauda equina syndrome. We report a 46-year-old female with obesity and a history of chronic back pain and radiculopathy who developed idiopathic Spinal epidural lipomatosis diagnosed by magnetic resonance imaging. The purpose of this report is to present a case of spinal epidural lipomatosis presenting with symptomatic cord compression and also remind this rare condition as a the differential diagnosis of epidural lesions in patients with risk factors.

Congenital diffuse infiltrating lipomatosis of the face (CDIL-F) is a rare clinicopathological entity with an unknown etiology, in which mature adipose tissue infiltrates the soft tissue structures in one side, and causes considerable asymmetry. Herein, we report a case of CDIL-F who underwent many surgical procedures without definite diagnosis during 12 years. CDIL-F presents symptoms with various severity levels due to infiltration of adipose tissue that makes removal difficult. Thus, it is recommended to inform patients about the high rate of recurrence.

Lipomatosis of the nerve, also known as fibrolipomatous hamartoma, is characterized by the infiltration of the nerve by fibro-fatty tissue. The affected nerve becomes thicker, and it simulates a mass lesion. Lipomatosis usually affects the median nerve and lipomatosis of the sciatic nerve is extremely rare. Magnetic resonance imaging (MRI) is the key to diagnosis, and it is usually pathognomonic.In this report, MRIand diffusion-weightedMRIfindings of a case of a giant sciatic nerve lipomatosis without macrodactyly are presented. The MRI findings are unique, and awareness of the MRI features of this rare soft tissue mass may prevent unnecessary biopsies and surgeries.

Background: Spinal epidural lipomatosis (SEL) is a rare disease, defined as diffuse hypertrophy of unencapsulated adipose tissue causing spinal canal compression and progressive neurologic deficits. However, there are few studies on SEL in Korea. Objectives: The purpose of this study was to describe the prevalence and clinical characteristics of SEL in Korea. Methods: Of the 3702 symptomatic patients (1575 males and 2127 females) who underwent lumbar spine magnetic resonance imaging (MRI) at the age of 20 years or older from January 2014 to December 2016, 42 patients (27 males and 15 females) diagnosed with SEL were selected. Medical records and telephone counseling were used to document sex, age, height, weight, clinical symptoms, coexistent spinal disease, accompanying diseases, and alcoholism and smoking status. One radiologist classified the severity of epidural lipomatosis into three grades from I to III according to Borre et al. We obtained four linear measurements at the axial plane parallel based in the narrowest on MRI image. Results: The incidence of SEL in the lumbar spine was 1. 1%, which was 1. 71% in men and 0. 7% in women. The mean age was 69. 4 ± 10. 9 years and the mean body mass index (BMI) was 26. 4 ± 3. 5 kg/m2. The most common clinical symptoms were lower back pain and radiating leg pain (26 patients, 61. 9%). The level of affected SEL was found to be most prevalent at L5-S1 (21 patients, 50%). Concomitant diseases were hypertension (26 patients, 61. 9%) and diabetes (12 patients, 28. 5%). The most common SEL grade was type III (21 patients, 50%), followed by types II (17 patients, 40. 4%) and I (4 patients, 9. 5%). Conclusions: Lumbar spine MRI at one hospital showed that the incidence of symptomatic SEL was 1. 1%; SEL is common at the L5-S1 level and in male patients, and severity grade is often severe.

Encephalocraniocutaneous lipomatosis (ECCL), also known as Haberland syndrome, is a rare, nonhereditary, nonprogressive congenital neurocutaneous syndrome with underlying ectodermal dysgenesis. The classic triad of this syndrome is central nervous system (CNS), ocular, and cutaneous involvement as unilateral lipomatous lesions of the scalp, neck, and face with ipsilateral brain anomalies and ipsilateral ocular choristoma. Herein, this study reports a case of a 2-year-old boy presented with status epilepticus for the first time. Intraspinal lipoma, arachnoid cyst, cerebral hemiatrophy, asymmetric hydrocephaly, choristoma, and corneal clouding were noted. This case fulfilled Moog’s clinical criteria for diagnosis of Haberland syndrome. Additionally, this study introduces linear and whorled nevoid hypermelanosis and cerebral periventricular white matter hyperintensity as novel manifestations of this syndrome.

Renal replacement lipomatosis of the kidney is a rare entity characterized by renal sinus and perirenal fat proliferation often caused by renal calculi. Most of the renal parenchyma is replaced by fat and the kidney is usually small, atrophic and nonfunctioning. We report magnetic resonance imaging and ultrasonography findings of a pregnant woman with xanthogranulomatous pyelonephritis and renal replacement lipomatosis coexisting in the same kidney.

Intestinal lipomatosis also known as lipohyperplasia is a rare disease. Diffuse infiltration of the fatty tissue mainly in the submucosal layer is characteristic. It is usually asymptomatic and found incidentally. We report a case of lipomatosis in the terminal ileum and ileocecal valve. Multidetector computed tomography (MDCT) with contrast enhancement showed fatty infiltration of the terminal ileum and ileocecal valve.

INTRODUCTION: Pelvic lipomatosis is a benign proliferation of adipose tissue predominantly in the pelvic retroperitoneum. Involvement of the bladder and ureter may cause bilateral hydroureteronephrosis and low capacity bladder. (1) We present the case report of a patient with pelvic lipomatosis causing bilateral hydroureteronephrosis with low capacity bladder managed by laparoscopy assisted ‘ U’ configuration bilateral ileal ureter.

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