Purpose: To report 14 cases of gelatinous drop-like corneal dystrophy (GDCD) for the first time in Iran.Material and methods: This is a case series of 14 patients who were diagnosed based on clinical characteristics and pathologic documentation.Results: Of 14 cases, 11 were female and 3 were male. Average age was 28.6 years. According to family trees, the predominant mode of inheritance was autosomal recessive, however 1 case was sporadic and 3 cases in a single family showed autosomal dominant inheritance pattern. Ten cases underwent surgery including superficial keratectomy (SK), lamellar keratoplasty (LK), and penetrating keratoplasty (PK). Cases were followed for 5-15 years (mean 8). Recurrence was the rule; one case underwent 4 PKs in one eye.Conclusion: GDCD is a rare autosomal recessive corneal dystrophy which causes early and severe visual loss in young adults. Recurrences complicate SK, LK, and PK. Surgical interventions (especially PK) should better be postponed as much as possible.