POLAND SYNDROME AND ASSOCIATION WITH ATRIAL SEPTAL DEFECT AND PULMONARY STENOSIS; A TWO CASE REPORT

Q: How can I download an article?

To download an article from SID, first log in to the site, search for the article title, and click on the 'Download Article' option.

Q: How can I download an ISI article?

To download an ISI article on SID, enter the keyword or article title in the search bar, view the relevant results, click on the desired article, and select the 'Download Article' option.

Q: How can I access the SID database?

To access the SID database, visit SID.ir, create an account, and log in to access scientific resources.

Q: Is downloading articles from SID free?

Some articles on SID are available for free, while others require payment. Details are specified on the article's page.

MARDANI KIVI M.; SALARI A.; ALIZADEH A.; HASHEMI MOTLAGH K.; SAHEB EKHTIARI KH.

مرکز اطلاعات علمی Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Journal Paper

Paper Information

Journal: Journal of Guilan University of Medical Sciences Year:2012 | Volume:21 | Issue:82 Page(s): 90-95

Download Full-Text

Persian Verion

View:

1,760

Download:

Cites:

Information Journal Paper

Title

POLAND SYNDROME AND ASSOCIATION WITH ATRIAL SEPTAL DEFECT AND PULMONARY STENOSIS; A TWO CASE REPORT

Author(s)

Keywords

HEART SEPTAL DEFECTQ2

ATRIALQ2

POLAND SYNDROMEQ2

PALMONARY VALVE STENOSISQ2

Abstract

Introduction: Congenital unilateral absence of pectoralis muscles in combination with ipsilateral brachysyndactyly is the most acceptable definition of POLAND SYNDROME. This very rare syndrome has been reported in association with various malignancies and deformities including cardiovascular anomalies. To our knowledge, pulmonary stenosis associated with Poland's syndrome has not been described previously in literature, and there are a few articles about ATRIAL septal defect (ASD) in combination with this syndrome either. We present the first report of POLAND SYNDROME associated with pulmonary valve stenosis and another case of POLAND SYNDROME with ASD. We discuss common etiologic factors of this rare syndrome.Case history: Case one: The first patient is a 23 month old boy with POLAND SYNDROME presentation such as absence of pectoralis major of right hemi-thorax, nipple and subcutaneous hypoplasia and ipsilateral brachysyndactyly. On physical examination, we found a systolic ejection sound in auscultation so that a complete cardiac evaluation was performed. Pulmonary stenosis with 7mm diameter was detected by Color-Doppler echocardiography.Case two: The second patient is a 5 year old girl presenting typical POLAND SYNDROME clinical manifestation. She has congenital right pectoralis major agenesis, Right upper position of nipple and areola was compared to left hemi-thorax, and an ipsilateral hypoplastic hand with syndactyly and short fingers. The 2-dimentional echocardiogram revealed that she is suffering from an Ostium Secundum ASD.Conclusion: Although POLAND SYNDROME is a rare congenital one, it is associated with numerous anomalies and malignancies in the reported articles. The two mentioned cases are the samples of cardiac anomalies associated with this very unique syndrome. According to critical situation of cardiovascular problems, performing a complete cardiovascular evaluation in addition to common medical-surgical treatments seems to be essential for patients with POLAND SYNDROME.

Cites

No record.

References

No record.

Cite

APA: Copy

MARDANI KIVI, M., SALARI, A., ALIZADEH, A., HASHEMI MOTLAGH, K., & SAHEB EKHTIARI, KH.. (2012). POLAND SYNDROME AND ASSOCIATION WITH ATRIAL SEPTAL DEFECT AND PULMONARY STENOSIS; A TWO CASE REPORT. JOURNAL OF GUILAN UNIVERSITY OF MEDICAL SCIENCES, 21(82), 90-95. SID. https://sid.ir/paper/39796/en

Vancouver: Copy

MARDANI KIVI M., SALARI A., ALIZADEH A., HASHEMI MOTLAGH K., SAHEB EKHTIARI KH.. POLAND SYNDROME AND ASSOCIATION WITH ATRIAL SEPTAL DEFECT AND PULMONARY STENOSIS; A TWO CASE REPORT. JOURNAL OF GUILAN UNIVERSITY OF MEDICAL SCIENCES[Internet]. 2012;21(82):90-95. Available from: https://sid.ir/paper/39796/en

IEEE: Copy

M. MARDANI KIVI, A. SALARI, A. ALIZADEH, K. HASHEMI MOTLAGH, and KH. SAHEB EKHTIARI, “POLAND SYNDROME AND ASSOCIATION WITH ATRIAL SEPTAL DEFECT AND PULMONARY STENOSIS; A TWO CASE REPORT,” JOURNAL OF GUILAN UNIVERSITY OF MEDICAL SCIENCES, vol. 21, no. 82, pp. 90–95, 2012, [Online]. Available: https://sid.ir/paper/39796/en

Related Journal Papers