PYLORIC ATRESIA ASSOCIATED WITH EPIDERMOLYSIS BULLOSA: A REPORT OF 4 SURVIVALS IN 5 CASES

Q: How can I download an article?

To download an article from SID, first log in to the site, search for the article title, and click on the 'Download Article' option.

Q: How can I download an ISI article?

To download an ISI article on SID, enter the keyword or article title in the search bar, view the relevant results, click on the desired article, and select the 'Download Article' option.

Q: How can I access the SID database?

To access the SID database, visit SID.ir, create an account, and log in to access scientific resources.

Q: Is downloading articles from SID free?

Some articles on SID are available for free, while others require payment. Details are specified on the article's page.

ALAM SAHEBPOUR A.R.; GHAFARI V.; SHOKOUHI L.

مرکز اطلاعات علمی Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Journal Paper

Paper Information

Journal: Iranian Journal of Pediatrics Year:2007 | Volume:17 | Issue:4 Page(s): 369-374

Download Full-Text

Persian Verion

View:

1,283

Download:

204

Cites:

Information Journal Paper

Title

PYLORIC ATRESIA ASSOCIATED WITH EPIDERMOLYSIS BULLOSA: A REPORT OF 4 SURVIVALS IN 5 CASES

Author(s)

ALAM SAHEBPOUR A.R. | GHAFARI V. | SHOKOUHI L. | Issue Writer Certificate

Keywords

PYLORIC ATRESIAQ3

EPIDERMOLYSIS BULLOSAQ3

GASTRODUODENOSTOMYQ3

SURGERYQ3

Abstract

Objective: PYLORIC ATRESIA (PA) is a rare congenital anomaly that constitutes approximately 1% of all intestinal atresias, and its incidence is approximately 1 in 100,000 live births. PA may occur as an isolated condition or associated with other abnormalities, the most common being Junctional EPIDERMOLYSIS BULLOSA (EB). Evidence suggests that PA-EB is a distinct entity. In this report, we present 5 cases of PYLORIC ATRESIA associated with Junctional EPIDERMOLYSIS BULLOSA, 4 of whom survived after SURGERY. Cases Presentation: Prospective evaluation of 5 patients with PYLORIC ATRESIA associated with EPIDERMOLYSIS BULLOSA undergoing therapeutic SURGERY. Biopsy of the fresh bulla was compatible with Junctional EB in all 5 patients. All patients underwent laparatomy after stabilization. Four neonates underwent GASTRODUODENOSTOMY, and one patient had excision of membrane and pyloroplasty. Out of 5 neonates, 4 survive and one died from fulminant septicemia 12 days after operation.Conclusion: Although association of PA with EB has been reported to be fatal, recently there have been encouraging reports of survival among these patients. These 5 patients underwent SURGERY and survived, and are doing well on follow up.

Cites

No record.

References

No record.

Cite

APA: Copy

ALAM SAHEBPOUR, A.R., GHAFARI, V., & SHOKOUHI, L.. (2007). PYLORIC ATRESIA ASSOCIATED WITH EPIDERMOLYSIS BULLOSA: A REPORT OF 4 SURVIVALS IN 5 CASES. IRANIAN JOURNAL OF PEDIATRICS, 17(4), 369-374. SID. https://sid.ir/paper/76101/en

Vancouver: Copy

ALAM SAHEBPOUR A.R., GHAFARI V., SHOKOUHI L.. PYLORIC ATRESIA ASSOCIATED WITH EPIDERMOLYSIS BULLOSA: A REPORT OF 4 SURVIVALS IN 5 CASES. IRANIAN JOURNAL OF PEDIATRICS[Internet]. 2007;17(4):369-374. Available from: https://sid.ir/paper/76101/en

IEEE: Copy

A.R. ALAM SAHEBPOUR, V. GHAFARI, and L. SHOKOUHI, “PYLORIC ATRESIA ASSOCIATED WITH EPIDERMOLYSIS BULLOSA: A REPORT OF 4 SURVIVALS IN 5 CASES,” IRANIAN JOURNAL OF PEDIATRICS, vol. 17, no. 4, pp. 369–374, 2007, [Online]. Available: https://sid.ir/paper/76101/en

Related Journal Papers