PAPILLON-LEFÈVRE SYNDROME: REPORT OF A RARE CASE

Q: How can I download an article?

To download an article from SID, first log in to the site, search for the article title, and click on the 'Download Article' option.

Q: How can I download an ISI article?

To download an ISI article on SID, enter the keyword or article title in the search bar, view the relevant results, click on the desired article, and select the 'Download Article' option.

Q: How can I access the SID database?

To access the SID database, visit SID.ir, create an account, and log in to access scientific resources.

Q: Is downloading articles from SID free?

Some articles on SID are available for free, while others require payment. Details are specified on the article's page.

AHMADINIA AMIRREZA; MOGHAREABED AHMAD; IZADI MOZHGAN

Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Journal Paper

Paper Information

Journal: JOURNAL OF ISFAHAN DENTAL SCHOOL Year:2013 | Volume:9 | Issue:1 Page(s): 107-113

Download Full-Text

مرکز اطلاعات علمی Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Persian Verion

View:

833

Download:

Cites:

Information Journal Paper

Title

PAPILLON-LEFÈVRE SYNDROME: REPORT OF A RARE CASE

Author(s)

AHMADINIA AMIRREZA | MOGHAREABED AHMAD | IZADI MOZHGAN | Issue Writer Certificate

Keywords

AGGRESSIVE PERIODONTITISQ3

CATHEPSIN CQ3

HYPERKERATOSISQ2

PAPILLON-LEFEVRE SYNDROMEQ3

Abstract

Introduction: PAPILLON-LEFEVRE SYNDROME is a rare autosomal recessive disorder. This syndrome is characterized by palmoplantar HYPERKERATOSIS, severe periodontal destruction and premature loss of primary and permanent teeth. The teeth erupt normally but due to the severe alveolar bone loss in both deciduous and permanent dentitions teeth are exfoliated within two or three years after eruption and by the age of 15 or 17 patients are usually edentulous. The identified genetic defect in this syndrome involves a mutation in the gene encoding CATHEPSIN C. An increased susceptibility to infection has also been reported in patient with this syndrome.Case Report: A 15-year-old girl was referred to the dental clinic, complaining of the mobility of permanent teeth. The patient had lost all the permanent teeth except for teeth 13, 14, 17, 23, 27, 37, 43, 44 and 47. The third molars were impacted. The patient had advanced periodontal disease and all the teeth had severe mobility. There was HYPERKERATOSIS at the palms and soles. She did not report a history of recurrent skin infections and liver abscesses. Complete blood count and liver tests were within the normal limits.Conclusion: Due to periodontal disease the dentists are often the first to diagnose this syndrome. Early diagnosis of PAPILLON-LEFEVRE SYNDROME can help preserve the permanent teeth by early institution of treatment, using a multidisciplinary approach. Dental treatment includes extraction of all deciduous teeth, professional prophylaxis, conventional periodontal therapy, systemic antibiotics, oral retinoids, complete dentures and implants.

Cites

No record.

References

No record.

Cite

APA: Copy

AHMADINIA, AMIRREZA, MOGHAREABED, AHMAD, & IZADI, MOZHGAN. (2013). PAPILLON-LEFÈVRE SYNDROME: REPORT OF A RARE CASE. JOURNAL OF ISFAHAN DENTAL SCHOOL, 9(1), 107-113. SID. https://sid.ir/paper/126482/en

Vancouver: Copy

AHMADINIA AMIRREZA, MOGHAREABED AHMAD, IZADI MOZHGAN. PAPILLON-LEFÈVRE SYNDROME: REPORT OF A RARE CASE. JOURNAL OF ISFAHAN DENTAL SCHOOL[Internet]. 2013;9(1):107-113. Available from: https://sid.ir/paper/126482/en

IEEE: Copy

AMIRREZA AHMADINIA, AHMAD MOGHAREABED, and MOZHGAN IZADI, “PAPILLON-LEFÈVRE SYNDROME: REPORT OF A RARE CASE,” JOURNAL OF ISFAHAN DENTAL SCHOOL, vol. 9, no. 1, pp. 107–113, 2013, [Online]. Available: https://sid.ir/paper/126482/en

Related Journal Papers