Red Cell Enzymopathies in Patients with Hemolytic Anemia in Southern Iran: Case Series

Q: How can I download an article?

To download an article from SID, first log in to the site, search for the article title, and click on the 'Download Article' option.

Q: How can I download an ISI article?

To download an ISI article on SID, enter the keyword or article title in the search bar, view the relevant results, click on the desired article, and select the 'Download Article' option.

Q: How can I access the SID database?

To access the SID database, visit SID.ir, create an account, and log in to access scientific resources.

Q: Is downloading articles from SID free?

Some articles on SID are available for free, while others require payment. Details are specified on the article's page.

Tahmasebi Lila; HAGHPANAH SEZANEH; REZAEI NARGES; KARIMI MEHRAN

مرکز اطلاعات علمی Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Journal Paper

Paper Information

Journal: IRANIAN JOURNAL OF PEDIATRIC HEMATOLOGY AND ONCOLOGY Year:2016 | Volume:6 | Issue:4 Page(s): 244-247

Download Full-Text

View:

245

Download:

115

Cites:

Information Journal Paper

Title

Red Cell Enzymopathies in Patients with Hemolytic Anemia in Southern Iran: Case Series

Author(s)

Tahmasebi Lila | HAGHPANAH SEZANEH | REZAEI NARGES | KARIMI MEHRAN | Issue Writer Certificate

Keywords

Hereditary enzymopathy

Hemolysis

Hemolytic anemia

Enzyme deficiency

Abstract

Background: Hereditary red cell enzyme disorders are a group of Non-immune/Spherocytic Hemolytic anemia, although these disorders are rare and they have not public health problems, the detection of these defects could help to physician in treatment and differential diagnosis. This study evaluated 5 enzymopathies in patients with Hereditary Non – immune/Spherocytic Hemolytic anemia (HNSHA) during one year. Materials and Methods: This cross-sectional study, evaluated 5 erythrocyte enzymes in 22 patients (mean age of 10 ± 9. 3) with Hereditary Non-immune/ Spherocytic Hemolytic anemia in Southern Iran from Jan 2014-Feb 2015. Evaluated erythrocyte enzymes consisted of pyruvate kinase (PK), G6PD, Catalase, Glutathion Proxidase( GP) and Glutathion Reductase( GR), all of these enzymes checked by quantitative assay except G6PD that evaluated by qualitative activity assay. The clinical and para clinical data were gathered from patient’ s documents. Results: Results showed that 2 patients were PK deficient (9. 1 %), 4 patients were G6PD deficient (18. 2%), 1patient was GP deficient (4. 5%), 1 patient was Catalase deficient (4. 5%) and there is no patient with GR deficiency. Conclusion: This study showed that enzymopathies should be into consideration in patients with non-immune Hemolytic anemia, if other common causes of Hemolysis such as hemoglobinopathies and membranopathies have been excluded.

Cites

No record.

References

No record.

Cite

APA: Copy

Tahmasebi, Lila, HAGHPANAH, SEZANEH, REZAEI, NARGES, & KARIMI, MEHRAN. (2016). Red Cell Enzymopathies in Patients with Hemolytic Anemia in Southern Iran: Case Series. IRANIAN JOURNAL OF PEDIATRIC HEMATOLOGY AND ONCOLOGY, 6(4), 244-247. SID. https://sid.ir/paper/320654/en

Vancouver: Copy

Tahmasebi Lila, HAGHPANAH SEZANEH, REZAEI NARGES, KARIMI MEHRAN. Red Cell Enzymopathies in Patients with Hemolytic Anemia in Southern Iran: Case Series. IRANIAN JOURNAL OF PEDIATRIC HEMATOLOGY AND ONCOLOGY[Internet]. 2016;6(4):244-247. Available from: https://sid.ir/paper/320654/en

IEEE: Copy

Lila Tahmasebi, SEZANEH HAGHPANAH, NARGES REZAEI, and MEHRAN KARIMI, “Red Cell Enzymopathies in Patients with Hemolytic Anemia in Southern Iran: Case Series,” IRANIAN JOURNAL OF PEDIATRIC HEMATOLOGY AND ONCOLOGY, vol. 6, no. 4, pp. 244–247, 2016, [Online]. Available: https://sid.ir/paper/320654/en

Related Journal Papers

No record.

Related Seminar Papers

No record.

Related Plans

No record.

Recommended Workshops