EMBRYONAL BILIARY ATRESIA WITH LEVOCARDIA AND SITUS INVERSUS: A CASE REPORT

Q: How can I download an article?

To download an article from SID, first log in to the site, search for the article title, and click on the 'Download Article' option.

Q: How can I download an ISI article?

To download an ISI article on SID, enter the keyword or article title in the search bar, view the relevant results, click on the desired article, and select the 'Download Article' option.

Q: How can I access the SID database?

To access the SID database, visit SID.ir, create an account, and log in to access scientific resources.

Q: Is downloading articles from SID free?

Some articles on SID are available for free, while others require payment. Details are specified on the article's page.

MOTAMED F.; ASHJAEI B.; SOBHANI MOHAMMAD

مرکز اطلاعات علمی Scientific Information Database (SID) - Trusted Source for Research and Academic Resources

Journal Paper

Paper Information

Journal: Iranian Journal of Pediatrics Year:2007 | Volume:17 | Issue:4 Page(s): 383-387

Download Full-Text

View:

319

Download:

126

Cites:

Information Journal Paper

Title

EMBRYONAL BILIARY ATRESIA WITH LEVOCARDIA AND SITUS INVERSUS: A CASE REPORT

Author(s)

MOTAMED F. | ASHJAEI B. | SOBHANI MOHAMMAD | Issue Writer Certificate

Keywords

EHBA

EXTRA HEPATIC BILIARY ATRESIA

MALFORMATION

SITUS INVERSUS

Abstract

Background: Biliary atresia (BA) is a rare disease and the end result of a destructive inflammatory process in bile ducts, leading to fibrosis and liver cirrhosis. It has two forms: 1) syndromic or fetal or embryonic (10-35%) with various congenital anomalies, 2) non syndromic (70-90%), in which BA is an isolated anomaly. In this article we report on an infant with the first form of BA in which diagnosis and operation was not based on routine liver biopsy but on associated MALFORMATIONs and clinical features that were highly suggestive of embryonal form of biliary atresia. Case Presentation: A 70-day old infant with syndromic BA, levocardia, SITUS INVERSUS and polysplenia. He developed jaundice in 4th day of life, liver was not palpable. Kasai operation was not effective. He developed liver cirrhosis at 3 months of age.Conclusion: Syndromic type of EHBA is a very rare disease with a worse outcome than non syndromic type of BA. Early diagnosis is important and may be difficult as the liver sometimes could not be palpable because of its malposition.

Cites

No record.

References

No record.

Cite

APA: Copy

MOTAMED, F., ASHJAEI, B., & SOBHANI, MOHAMMAD. (2007). EMBRYONAL BILIARY ATRESIA WITH LEVOCARDIA AND SITUS INVERSUS: A CASE REPORT. IRANIAN JOURNAL OF PEDIATRICS, 17(4), 383-387. SID. https://sid.ir/paper/550143/en

Vancouver: Copy

MOTAMED F., ASHJAEI B., SOBHANI MOHAMMAD. EMBRYONAL BILIARY ATRESIA WITH LEVOCARDIA AND SITUS INVERSUS: A CASE REPORT. IRANIAN JOURNAL OF PEDIATRICS[Internet]. 2007;17(4):383-387. Available from: https://sid.ir/paper/550143/en

IEEE: Copy

F. MOTAMED, B. ASHJAEI, and MOHAMMAD SOBHANI, “EMBRYONAL BILIARY ATRESIA WITH LEVOCARDIA AND SITUS INVERSUS: A CASE REPORT,” IRANIAN JOURNAL OF PEDIATRICS, vol. 17, no. 4, pp. 383–387, 2007, [Online]. Available: https://sid.ir/paper/550143/en

Related Journal Papers

No record.

Related Seminar Papers

No record.

Related Plans

No record.

Recommended Workshops